Introduction — This topic includes links to society and government-sponsored guidelines from selected countries and regions around the world. We will update these links periodically; newer versions of some guidelines may be available on each society's website. Some societies may require users to log in to access their guidelines.
The recommendations in the following guidelines may vary from those that appear in UpToDate topic reviews. Readers who are looking for UpToDate topic reviews should use the UpToDate search box to find the relevant content.
Links to related guidelines are provided separately.
●(See "Society guideline links: Hemoptysis".)
●(See "Society guideline links: Nontuberculous mycobacteria".)
●(See "Society guideline links: Pediatric liver disease".)
●(See "Society guideline links: Chronic pancreatitis and pancreatic exocrine insufficiency".)
●(See "Society guideline links: Lung transplantation".)
●(See "Society guideline links: Bronchiectasis".)
●(See "Society guideline links: Portal hypertension and ascites".)
International
●International Society for Pediatric and Adolescent Diabetes (ISPAD): Clinical practice consensus guidelines for the management of cystic fibrosis-related diabetes in children and adolescents (2022)
●European Society for Paediatric Gastroenterology, Hepatology, and Nutrition (ESPGHAN) and North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition (NASPGHAN): Nutritional considerations in pediatric pancreatitis (2018)
●International Committee on Mental Health in Cystic Fibrosis (ICMH-CF): Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus statements for screening and treating depression and anxiety (2016)
●ESPGHAN and NASPGHAN: Clinical report on the assessment of exocrine pancreatic function and pancreatitis in children (2015)
United States
●Cystic Fibrosis Foundation (CFF): Clinical care guidelines
•Age-specific care guidelines
•CFTR modulator therapy care guidelines
•Diagnosis clinical care guidelines
•Infection prevention and control care guidelines
•Nutrition and GI care guidelines
•Other CF-related conditions care guidelines
•Respiratory care guidelines
•Screening and treating depression and anxiety guidelines
●CFF: Consensus recommendations on cystic fibrosis screening, evaluation, and management of hepatobiliary disease (2023)
●Academy of Nutrition and Dietetics (AND): Cystic fibrosis (CF) guideline (2020)
●AND: CF – Guideline recommendations and supporting evidence (2020)
●CFF: Consensus guidelines for the care of individuals with advanced cystic fibrosis lung disease (2020)
●Cystic Fibrosis Colorectal Cancer Screening Task Force: Cystic fibrosis colorectal cancer screening consensus recommendations (2017)
●CFF and European Cystic Fibrosis Society (ECFS): Consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis (2015)
●American Thoracic Society (ATS): An official workshop report on optimal lung function tests for monitoring cystic fibrosis, bronchopulmonary dysplasia, and recurrent wheezing in children less than 6 years of age (2013)
●American Diabetes Association (ADA) and CFF: Clinical care guidelines for cystic fibrosis-related diabetes (2010)
Europe
●European Respiratory Society (ERS)/Thoracic Society of Australia and New Zealand (TSANZ): Statement on the management of reproduction and pregnancy in women with airways diseases (2020)
●European Cystic Fibrosis Society (ECFS): Best practice guidelines (2018)
●European Society for Paediatric Gastroenterology, Hepatology, and Nutrition (ESPGHAN) and North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition (NASPGHAN): Nutritional considerations in pediatric pancreatitis (2018)
●Cystic Fibrosis Foundation (CFF) and ECFS: Consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis (2016)
●ERS/ECFS: Report on the care of adults with cystic fibrosis (2016)
●European Society for Clinical Nutrition and Metabolism (ESPEN)-ESPGHAN-ECFS: Guidelines on nutrition care for infants, children, and adults with cystic fibrosis (2016)
●ESPGHAN and NASPGHAN: Clinical report on the assessment of exocrine pancreatic function and pancreatitis in children (2015)
●ECFS: Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease (2011)
●ECFS: End of life care for patients with cystic fibrosis (2011)
●ECFS: European cystic fibrosis bone mineralisation guidelines (2011)
●ECFS: Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patients (2011)
●ECFS: Guiding principles on how to manage relevant psychological aspects within a CF team – Interdisciplinary approaches (2011)
●ESPGHAN: Defining DIOS and constipation in cystic fibrosis with a multicentre study on the incidence, characteristics, and treatment of DIOS (2010)
●ECFS: European best practice guidelines for cystic fibrosis neonatal screening
●ECFS: Guidelines for the management of pregnancy in women with cystic fibrosis (2008)
United Kingdom
●Cystic Fibrosis Trust: Consensus documents
●National Institute for Health and Care Excellence (NICE): Quality standard on cystic fibrosis (2018)
●NICE: Guideline on cystic fibrosis – Diagnosis and management (2017)
●Royal College of Paediatrics and Child Health (RCPCH): Guidelines for the performance of the sweat test for the investigation of cystic fibrosis in the UK, 2nd version (2014)
Australia–New Zealand
●European Respiratory Society (ERS)/Thoracic Society of Australia and New Zealand (TSANZ): Statement on the management of reproduction and pregnancy in women with airways diseases (2020)
●TSANZ: Position paper on work environment risks for health care workers with cystic fibrosis (2018)
●TSANZ: Nutrition guidelines for cystic fibrosis in Australia and New Zealand (2017)
●TSANZ: Clinical practice guideline for physiotherapy for cystic fibrosis in Australia and New Zealand (2016)
●Asian Pacific Society of Respirology (APSR): Clinical practice guideline on Australian standards of care for cystic fibrosis-related diabetes (2013)
●Cystic Fibrosis Australia: Cystic fibrosis standards of care, Australia (2008)
