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World Kidney Day 2023: preparing for the unexpected, supporting the vulnerable!
Ankana Daga, Erica C. Bjornstad, Florencio McCarthy & Melvin Bonilla-Felix
doi : 10.1007/s00467-023-05945-7
Volume 38, issue 6, June 2023
How common is chronic kidney disease in children with lupus nephritis?
Scott E. Wenderfer, Alvaro Orjuela & Janis Dionne
Diagnosis and treatment of IgA nephropathy and IgA vasculitis nephritis in Chinese children
Xuhui Zhong & Jie Ding
doi : 10.1007/s00467-022-05798-6
IgA nephropathy (IgAN) and IgA vasculitis-associated nephritis (IgAVN) are among the most frequent childhood glomerular diseases and are characterized by significant variability in clinical manifestations, pathological presentation and long-term outcomes. IgAVN, alternatively called purpura nephritis, is pathologically indistinguishable from kidney-limited IgAN.
Phthalates cause a low-renin phenotype commonly found in premature infants with idiopathic neonatal hypertension
Randall D. Jenkins
doi : 10.1007/s00467-022-05773-1
Since the 1970s, when the initial reports of neonatal hypertension related to renal artery thromboembolism were published, other secondary causes of neonatal hypertension have been reported. Those infants with no identifiable cause of hypertension were labeled with a variety of terms.
Kidney tubular injury induced by valproic acid: systematic literature review
Giulia Anguissola, Dennis Leu, Giacomo D. Simonetti, Barbara Goeggel Simonetti, Sebastiano A. G. Lava, Gregorio P. Milani, Mario G. Bianchetti & Martin Scoglio
doi : 10.1007/s00467-022-05869-8
Valproic acid is prescribed for epilepsy and as prophylaxis for bipolar disorder and migraine headaches. It has also been implicated as a cause of a kidney tubular injury.
Point-of-care ultrasound in pediatric nephrology
Sidharth Kumar Sethi, Rupesh Raina, Abhilash Koratala, Afagh Hassanzadeh Rad, Ananya Vadhera & Hamidreza Badeli
doi : 10.1007/s00467-022-05729-5
Point-of-care ultrasound (POCUS) has evolved in recent years in clinical practice, helping in early bedside diagnosis of important etiologies. Many medical schools and training programs are integrating POCUS into their curriculum.
Hypogammaglobulinemia in pediatric kidney transplant recipients
Victoria Dimitriades & Lavjay Butani
doi : 10.1007/s00467-022-05757-1
Infections remain the most common cause of hospitalization after kidney transplantation, contributing to significant post-transplant morbidity and mortality.
A case of persistent hypertension in a 6-year-old: Questions
Mugdha Rairikar & Elizabeth Anyaegbu Onugha
A case of persistent hypertension in a 6-year-old: Answers
Mugdha Rairikar & Elizabeth Anyaegbu Onugha
A child with abdominal pain, arthralgia, palpable skin rash, hepatosplenomegaly, and pancytopenia: Questions
Subhankar Sarkar, Niladri Bose, Deblina Dasgupta, Shakil Akhtar & Rajiv Sinha
A child with abdominal pain, arthralgia, palpable skin rash, hepatosplenomegaly, and pancytopenia: Questions
Subhankar Sarkar, Niladri Bose, Deblina Dasgupta, Shakil Akhter & Rajiv Sinha
Kidney impairment in a child with acute-subacute paracoccidioidomycosis: Questions
Mariana Tresoldi das Neves Romaneli, Sumara Pinto Zuanazzi, Leandro Luiz Lopes de Freitas, Vera Maria Santoro Belangero, Antonia Teresinha Tresoldi & Ricardo Mendes Pereira
Kidney impairment in a child with acute-subacute paracoccidioidomycosis: Answers
Mariana Tresoldi das Neves Romaneli, Sumara Pinto Zuanazzi, Leandro Luiz Lopes de Freitas, Vera Maria Santoro Belangero, Antonia Teresinha Tresoldi & Ricardo Mendes Pereira
Predictive factors for survival in patients with oligohydramnios secondary to antenatal kidney disease
Mathilde Baudin, Claire Herbez, Isabelle Guellec, Ferdinand Dhombres, Lucie Guilbaud, Cyrielle Parmentier, Jean Daniel Delbet, Catherine Garel, Eleonore Bondiaux, Jean Marie Jouannic & Tim Ulinski
doi : 10.1007/s00467-022-05800-1
Renal oligohydramnios (ROH) is caused by bilateral congenital abnormalities, either of renal parenchymal or obstructive origin. ROH is a poor prognostic factor of neonatal survival; lung hypoplasia is reported to be the main cause of mortality. We aimed to describe the fetal morbidity and pre- and postnatal mortality in case of ROH due to renal congenital pathologies and to find predictive risk factors for morbidity and mortality.
Shared genetic risk across different presentations of gene test–negative idiopathic nephrotic syndrome
Mallory L. Downie, Sanjana Gupta, Melanie M. Y. Chan, Omid Sadeghi-Alavijeh, Jingjing Cao, Rulan S. Parekh, Carmen Bugarin Diz, Agnieszka Bierzynska, Adam P. Levine, Ruth J. Pepper, Horia Stanescu, Moin A. Saleem, Robert Kleta, Detlef Bockenhauer, Ania B. Koziell & Daniel P. Gale
doi : 10.1007/s00467-022-05789-7
Idiop athic nephrotic syndrome (INS) is classified in children according to response to initial corticosteroid therapy into steroid-sensitive (SSNS) and steroid-resistant nephrotic syndrome (SRNS), and in adults according to histology into minimal change disease (MCD) and focal segmental glomerulosclerosis (FSGS).
Clinical and molecular characterization of a large primary hyperoxaluria cohort from Saudi Arabia: a retrospective study
Majid Alfadhel, Muhammad Umair, Malak A. Alghamdi, Khalid Al Fakeeh, Abdullah T. Al Qahtani, Afrah Farahat, Mohamed A. Shalaby, Jameela A. Kari, Rupesh Raina, Pierre Cochat & Khalid A. Alhasan
doi : 10.1007/s00467-022-05784-y
Primary hyperoxalurias (PHs) constitute rare disorders resulting in abnormal glyoxalate metabolism. PH-associated phenotypes range from progressive nephrocalcinosis and/or recurrent urolithiasis to early kidney failure.
Long-term outcomes after pre-emptive liver transplantation in primary hyperoxaluria type 1
Hadas Shasha-Lavsky, Aviv Avni, Ziv Paz, Limor Kalfon, Amiel A. Dror, Orly Yakir, Tzipora Falik Zaccai & Irith Weissman
doi : 10.1007/s00467-022-05803-y
Primary hyperoxaluria type 1 (PH1) is an autosomal recessive disease caused by the liver defect of oxalate metabolism, which leads to kidney failure and systemic manifestations. Until recently, liver transplantation was the only definitive treatment.
Utility of muscle ultrasound in nutritional assessment of children with nephrotic syndrome
Mona Hamed Gehad, Yousif Mohamed Yousif, Maha Ibrahim Metwally, Amany Mohammed AbdAllah, Lamiaa Lotfy Elhawy, Amal S. El-Shal & Ghada Mohammed Abdellatif
doi : 10.1007/s00467-022-05776-y
Nutritional status assessment in children with nephrotic syndrome (NS) is critical for identifying patients who are at risk of protein-energy wasting (PEW) and for determining their nutritional needs and monitoring nutritional intervention outcomes.
Mizoribine halts kidney fibrosis in childhood IgA nephropathy: association with modulation of M2-type macrophages
Yohei Ikezumi, Masatoshi Yoshikane, Tomomi Kondoh, Yuji Matsumoto, Naonori Kumagai, Masahiro Kaneko, Hiroya Hasegawa, Takeshi Yamada, Toshiaki Suzuki & David J. Nikolic-Paterson
doi : 10.1007/s00467-022-05786-w
The immunosuppressant mizoribine (Miz) can reduce progression of childhood IgA nephropathy (IgAN). This study examined whether Miz affects CD163+ M2-type macrophages which are associated with kidney fibrosis in childhood IgAN.
Chronic kidney disease in patients with childhood-onset systemic lupus erythematosus
Ana P. Sakamoto, Clovis A. Silva, Aline G. Islabão, Glaucia V. Novak, Beatriz Molinari, Paulo K. Nogueira, Rosa M. R. Pereira, Claudia Saad-Magalhães, Gleice Clemente, Daniela P. Piotto, Nadia E. Aikawa, Ana C. Pitta, Vitor C. Trindade, Simone Appenzeller, Luciana M. Carvalho, Carlos N. Rabelo-Junior, Adriana R. Fonseca, Flavio R. Sztajnbok, Maria C. Santos, Blanca E. Bica, Evaldo G. Sena, Ana J. Moraes, Melissa M. Fraga, Teresa C. Robazzi, for the Brazilian Childhood-onset Systemic Lupus Erythematosus Registry Group
doi : 10.1007/s00467-022-05811-y
Lupus nephritis (LN) is a frequent manifestation of childhood-onset systemic lupus erythematosus (cSLE) with a potential risk for kidney failure and poor outcomes. This study aimed to evaluate stages III, IV, and V of chronic kidney disease (CKD) and investigate risk factors for CKD in cSLE patients.
Fetal growth restriction followed by very preterm birth is associated with smaller kidneys but preserved kidney function in adolescence
Jonas Liefke, Caroline Heijl, Katarina Steding-Ehrenborg, Eva Morsing, Håkan Arheden, David Ley & Erik Hedström
doi : 10.1007/s00467-022-05785-x
Preterm birth and fetal growth restriction (FGR) are associated with structural and functional kidney changes, increasing long-term risk for chronic kidney disease and hypertension. However, recent studies in preterm children are conflicting, indicating structural changes but normal kidney function. This study therefore assessed kidney structure and function in a cohort of adolescents born very preterm with and without verified FGR.
Relation between obesity-related comorbidities and kidney function estimation in children
Mark J. C. M. van Dam, Hans Pottel & Anita C. E. Vreugdenhil
doi : 10.1007/s00467-022-05810-z
The current childhood obesity pandemic is likely to result in an increased risk of chronic kidney disease (CKD) later in life. Correlations between obesity-related comorbidities and kidney function can be found, but it is unclear to what extent this is caused by bias due to different mathematical forms of the estimated glomerular filtration rate (eGFR) equations.
Normative values of renin and aldosterone in clinically stable preterm neonates
James Haiyang Xu, Erika Bariciak, Mary-Ann Harrison, Margaret Broom, Brigitte Lemyre, Richard J. Webster, Gabrielle Weiler, Jane E. Dahlstrom & Alison Kent
doi : 10.1007/s00467-022-05807-8
There is a paucity of literature on the normative levels of plasma renin concentration (PRC) and serum aldosterone (SA) in premature neonates. This study aims to provide normative data on PRC and SA levels in preterm neonates in the first 2Â weeks after birth and explore associations with maternal, perinatal, or postnatal factors.
Alterations in diastolic function and cardiac geometry in children: a longitudinal study across the spectrum of dialysis and transplant
Kristen Sgambat, Sarah Clauss & Asha Moudgil
doi : 10.1007/s00467-022-05771-3
Children with kidney failure have increased risk for cardiovascular morbidities before and after transplantation. Ejection fraction is often preserved, masking cardiac dysfunction until severe. Data on longitudinal changes in diastolic function and cardiac geometry are limited.
Health-related quality of life amongst children with chronic kidney disease in Malaysia: performance of the Bahasa Melayu version of the PedsQL 3.0 ESRD Module
Kamila Abu Bakar, Nor Asiah Muhamad, Mohamad Alwi Sarpin, Syaniza Shaharudin, Sangeet Sidhu, Suet Li Yap, Tengku Hasnita Tengku Hussain, Hai Liang Tan, Fen Ni Ong, Wen Chian Gan, Mohammad Ikram Ilias, Juliana Othman & Caroline Siew Yin Eng
doi : 10.1007/s00467-022-05774-0
The PedsQL 3.0 End Stage Renal Disease (ESRD) Module is a well-accepted instrument internationally but it is not available in the local language. We aimed to validate the Bahasa Melayu (Malay language) version and determine the health-related quality of life (HRQoL) scores amongst children with CKD in Malaysia.
Changes in bone biomarkers in response to different dosing regimens of cholecalciferol supplementation in children with chronic kidney disease
Nivedita Kamath, Arpana Iyengar, Hamsa V. Reddy, Jyoti Sharma, Jyoti Singhal, Sudha Ekambaram, Susan Uthup, Sumithra Selvam, Mandy Wan, Anja Rahn, Dagmar Christiane-Fischer & Rukshana Shroff
doi : 10.1007/s00467-022-05790-0
The effect of different dosing regimens of cholecalciferol supplementation on bone biomarkers has not been studied in children with chronic kidney disease (CKD).
The cost of hospitalizations for treatment of hemodialysis catheter-associated blood stream infections in children: a retrospective cohort study
Heather L. Wasik, Alicia Neu, Bradley Warady, Brendan Crawford, Troy Richardson, Heidi G. De Souza, Diana Cardwell & Rebecca Ruebner
doi : 10.1007/s00467-022-05764-2
Hospitalization costs for treatment of hemodialysis (HD) catheter-associated blood stream infections (CA-BSI) in adults are high. No studies have evaluated hospitalization costs for HD CA-BSI in children or identified factors associated with high-cost hospitalizations.
Left ventricular hypertrophy in pediatric patients on maintenance dialysis: a report of the North American Pediatric Renal Transplant Cooperative Study (NAPRTCS)
Kyle Merrill, Shirley Galbiati & Mark Mitsnefes on behalf of the NAPRTCS Investigators
doi : 10.1007/s00467-022-05796-8
Cardiovascular disease is the leading cause of death in pediatric patients with kidney failure. Left ventricular hypertrophy (LVH) is recognized as the most common cardiovascular abnormality in these patients.
Humoral immune response and live-virus neutralization of the SARS-CoV-2 omicron (BA.1) variant after COVID-19 mRNA vaccination in children and young adults with chronic kidney disease
Maximilian Stich, Veronica Di Cristanziano, Burkhard Tönshoff, Lutz Thorsten Weber, Jörg Dötsch, Marian Theodor Rammer, Susanne Rieger, Eva Heger, Sven F. Garbade, Kathrin Burgmaier, Louise Benning, Claudius Speer, Sandra Habbig & Sophie Haumann
doi : 10.1007/s00467-022-05806-9
Data on humoral immune response to standard COVID-19 vaccination are scarce in adolescent patients and lacking for children below 12Â years of age with chronic kidney disease including kidney transplant recipients.
Differences in medication adherence between preemptive and post-dialysis young kidney transplant recipients
Yulia Vaisbourd, Mourad Dahhou, Alexia De Simone, Xun Zhang & Bethany J. Foster
doi : 10.1007/s00467-022-05797-7
The mechanisms underlying the superior graft survival associated with preemptive kidney transplantation, compared with transplantation following a period of dialysis, are unknown. We aimed to compare medication adherence between preemptively transplanted young kidney transplant recipients and those who received a transplant after an interval of dialysis.
Risk factors for neurocognitive impairment and the relation with structural brain abnormality in children and young adults with severe chronic kidney disease
Sophie Lijdsman, Kim J. Oostrom, Marit S. van Sandwijk, Antonia H. Bouts, Koen van Hoeck, Huib de Jong, Jaap Oosterlaan, Frederike J. Bemelman, Marsh Königs & Jaap W. Groothoff
doi : 10.1007/s00467-022-05781-1
Severe chronic kidney disease (CKD) in children and young adults has shown to be associated with abnormal brain development, which may contribute to neurocognitive impairments. We aimed to investigate risk factors for neurocognitive impairment and investigate the relation with structural brain abnormalities in young severe CKD patients.
Acute kidney injury and early fluid load in a retrospective cohort of neonatal sepsis
Faris N. Al Gharaibeh, Shruthi Mohan, Michael A. Santoro, Cara L. Slagle & Stuart L. Goldstein
doi : 10.1007/s00467-022-05840-7
Sepsis and acute kidney injury (AKI) are associated with mortality in the newborn intensive care unit (NICU). There is a paucity of studies that describe AKI and fluid overload in neonatal sepsis and their association with mortality.
Severe rhabdomyolysis secondary to COVID-19 mRNA vaccine in a teenager
Aidan Pucchio, Maya Heled Akiva, Helena Evangeliou, Jesse Papenburg & Marina I. Salvadori
doi : 10.1007/s00467-022-05808-7
Rhabdomyolysis, the breakdown of skeletal muscles following an insult or injury, has been established as a possible complication of SARS-CoV-2 infection. Despite being highly effective in preventing COVID-19-related morbidity and mortality, several cases of COVID-19 mRNA vaccination-induced rhabdomyolysis have been identified. We provide the second description of a pediatric case of severe rhabdomyolysis presenting after COVID-19 mRNA vaccination.
Simultaneous kidney and pancreas transplantation in a patient with nail-patella syndrome and insulin-dependent diabetes
Peter Sloane, Janel Darcy Hunter, Jen-Jar Lin & Ashton Chen
doi : 10.1007/s00467-022-05817-6
Nail-patella syndrome (NPS) is a rare autosomal dominant disorder caused by a mutation in LIM-homeodomain transcription factor 1-beta (LMX1B) and characterized by nail dystrophy, skeletal changes, glaucoma, and kidney disease with up to 30% of patients progressing to kidney failure. Autoimmune diseases, including thyroid disease, have been reported previously in patients with NPS.
Diagnosing SARS-CoV-2 vaccination-related rhabdomyolysis requires the exclusion of all differential causes
Josef Finsterer & Fulvio A. Scorza
Response to Finsterer and Scorza
Marina I. Salvadori, Aidan Pucchio, Maya Heled Akiva, Helena Evangeliou & Jesse Papenburg
