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Renal angiomyolipoma staging criteria proposed by University Medical Center Utrecht

Renal angiomyolipoma staging criteria proposed by University Medical Center Utrecht
Stage Number of angiomyolipoma Angiomyolipoma size Description of kidney anatomy
None detected* None ≥1 cm in longest diameter Normal
1 ≤5 <3.5 cm Normal
2 >5 <3.5 cm Normal
3 ≤5 At least 1 ≥3.5 cm Kidney intact
4 >5 1 to 4 ≥3.5 cm Kidney intact
5 >5 ≥5 ≥3.5 cm Kidney recognizable
6 >5 At least 1 ≥5 cm Kidney not recognizable
* Angiomyolipoma not detectable or lesions <1 cm unidentifiable as angiomyolipoma.
Reproduced from: Eijkemans MJ, van der Wal W, Reijnders LJ, et al. Long-term follow-up assessing renal angiomyolipoma treatment patterns, morbidity, and mortality: An observational study in tuberous sclerosis complex patients in the Netherlands. Am J Kidney Dis 2015; 66:638. Table used with the permission of Elsevier Inc. All rights reserved.
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