Type of cutaneous lymphoma | Frequency of CD8 expression (%) | Helpful distinguishing features |
Aggressive epidermotropic CD8+ cytotoxic CTCL | 100 | Ulcerating plaques, nodules and tumors, no prior or concurrent eczematous patches/plaques |
Early patch/plaque-stage MF | ~15 | Prior or concurrent eczematous patches/plaques* |
Tumor-stage/transformed MF | ~5 | (Ulcerating) tumors, prior or concurrent eczematous patches/plaques* |
Pagetoid reticulosis | ~50 | Solitary, slowly expanding plaque usually on the extremities |
C-ALCL | <5 | Solitary or localized (ulcerating) tumors, tendency to spontaneous remission* |
LyP, type D | 100 | Recurrent self-healing popular, nodular or ulceronecrotic skin lesions* |
SPTCL | >90 | Subcutaneous nodules and plaques, no ulceration, no epidermal involvement |
Primary cutaneous acral CD8+ T cell lymphoproliferative disorder | 100 | Slowly progressive nodule on ear and other acral sites, no ulceration, no epidermal involvement, low proliferation rate |
C-ALCL: cutaneous anaplastic large cell lymphoma; CTCL: cutaneous T cell lymphoma; LyP: lymphomatoid papulosis; MF: mycosis fungoides; SPTCL: subcutaneous panniculitis-like T cell lymphoma.
* No difference in clinical presentation and prognosis between CD8+ and more common CD4+ cases.آیا می خواهید مدیلیب را به صفحه اصلی خود اضافه کنید؟