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خرید پکیج
تعداد آیتم قابل مشاهده باقیمانده : 3 مورد
نسخه الکترونیک
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Causes of cystic lung disease in adults*

Causes of cystic lung disease in adults*
Amyloidosis
Bronchopulmonary dysplasia (lung cysts likely a consequence of infection)
Congenital/genetic (eg, Birt-Hogg-Dubé syndrome, Down syndrome, neurofibromatosis, Proteus syndrome)
Erdheim Chester disease
Fire-eater's lung
Fungi (eg, coccidioidomycosis, Pneumocystic jirovecii)
Hypersensitivity pneumonitis
Hyper immunoglobulin-E syndrome (due to recurrent staphylococcal pneumonia)
Light chain deposition diseaseΔ
Lymphangioleiomyomatosis (sporadic or related to tuberous sclerosis complex)
Lymphoid interstitial pneumonia (eg, associated with Sjögren's disease, immunodeficiency)
Paragonimiasis
Primary and metastatic tumors (eg, lung adenocarcinoma, metastatic gastrointestinal and genitourinary adenocarcinoma, lymphoma, mesenchymal cystic hamartoma, metastatic sarcomas, pleuropulmonary blastoma)
Recurrent respiratory papillomatosis (involving lung parenchyma in adult)
Sjögren's disease (eg, due to Light chain deposition disease or lymphoid interstitial pneumonia)
Smoking-related interstitial lung disease (desquamative interstitial pneumonia, pulmonary Langerhans cell histiocytosis, respiratory bronchiolitis interstitial lung disease)
Smoking-related small airways injury
Staphylococcal pneumonia

* The four most common causes are identified in bold.

¶ Typically, cystic lung disease caused by amyloid is immunoglobulin light chain (AL) amyloid and may be seen in combination with Sjögren's disease. Amyloid fibrils are positive on Congo red stain and have green birefringence under polarized light.

Δ Light chain deposition disease (LCDD) does not have beta-pleated sheet configuration so it is negative on Congo red staining and does not have green birefringence under polarized light.

◊ May be associated with follicular bronchiolitis.
Graphic 113736 Version 4.0

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