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Consensus classification of pediatric Behçet syndrome

Consensus classification of pediatric Behçet syndrome
Item Description Value/item
Recurrent oral aphthosis At least three attacks/year 1
Genital ulceration or aphthosis Typically with scar 1
Skin involvement Necrotic folliculitis, acneiform lesions, erythema nodosum 1
Ocular involvement Anterior uveitis, posterior uveitis, retinal vasculitis 1
Neurologic signs With the exception of isolated headaches 1
Vascular signs Venous thrombosis, arterial thrombosis, arterial aneurysm 1
Three of six items are required to classify a patient as having pediatric Behçet syndrome.
Reproduced with permission from: Koné-Paut I, Shahram F, Darce-Bello M, et al. Consensus classification criteria for paediatric Behçet's disease from a prospective observational cohort: PEDBD. Ann Rheum Dis 2016; 75:958-64. Copyright © 2016 BMJ Publishing Group Ltd.
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