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2012 Chapel Hill Consensus Conference (CHCC) nomenclature of vasculitides for systemic vasculitis

2012 Chapel Hill Consensus Conference (CHCC) nomenclature of vasculitides for systemic vasculitis
Large-vessel vasculitis
  • Giant cell (temporal) arteritis
  • Takayasu arteritis
Medium-vessel vasculitis
  • Polyarteritis nodosa
  • Kawasaki disease
Small-vessel vasculitis
  • Antineutrophil cytoplasmic antibody-associated vasculitis
    • Microscopic polyangiitis
    • Granulomatosis with polyangiitis 
    • Eosinophilic granulomatosis with polyangiitis – previously Churg-Strauss syndrome
  • Immune complex small-vessel vasculitis
    • Antiglomerular basement membrane disease
    • Cryoglobulinemic vasculitis
    • IgA vasculitis (Henoch-Schönlein purpura)
    • Hypocomplementemic urticarial vasculitis
Variable-vessel vasculitis
  • Behçet syndrome
  • Cogan syndrome
Single-organ vasculitis
Vasculitis associated with a systemic disease
Vasculitis associated with probable etiology
IgA: immunoglobulin A.
Modified from: from: Jennette JC, Falk RJ, Bacon, PA et al. 2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides. Arthritis Rheum 2013; 65:1. http://onlinelibrary.wiley.com/wol1/doi/10.1002/art.37715/abstract. Copyright © 2013 American College of Rheumatology. Reproduced with permission of John Wiley & Sons Inc. This image has been provided by or is owned by Wiley. Further permission is needed before it can be downloaded to PowerPoint, printed, shared or emailed. Please contact Wiley's permissions department either via email: [email protected] or use the RightsLink service by clicking on the 'Request Permission' link accompanying this article on Wiley Online Library (http://onlinelibrary.wiley.com).
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