Predominately large vessel |
Takayasu arteritis |
Predominately medium-sized vessel |
Childhood polyarteritis nodosa |
Cutaneous polyarteritis nodosa |
Kawasaki disease |
Predominately small vessel |
Granulomatous |
Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome) |
Granulomatosis with polyangiitis |
Nongranulomatous |
Microscopic polyangiitis |
IgA vasculitis (Henoch-Schönlein purpura) |
Isolated cutaneous leukocytoclastic vasculitis |
Hypocomplementemic urticarial vasculitis |
Other vasculitides |
Behçet syndrome |
Secondary vasculitides due to infection, malignancy, or drugs, including hypersensitivity vasculitis |
Isolated vasculitis of the central nervous system |
Cogan's syndrome |
Unclassified |
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