Society guideline links: Pulmonary hypertension in children

Introduction — 

This topic includes links to society and government-sponsored guidelines from selected countries and regions around the world. We will update these links periodically; newer versions of some guidelines may be available on each society's website. Some societies may require users to log in to access their guidelines.

The recommendations in the following guidelines may vary from those that appear in UpToDate topic reviews. Readers who are looking for UpToDate topic reviews should use the UpToDate search box to find the relevant content.

Links to related guidelines are provided separately. (See "Society guideline links: Pulmonary hypertension in adults" and "Society guideline links: Heart failure in children" and "Society guideline links: Bronchopulmonary dysplasia".)

International

●Seventh World Symposium on Pulmonary Hypertension (WSPH): Definition, classification and diagnosis of pulmonary hypertension (2024)

●Seventh WSPH: Embracing the challenges of neonatal and paediatric pulmonary hypertension (2024)

●International Society for Heart and Lung Transplantation (ISHLT): Consensus statement for perioperative management of patients with pulmonary hypertension and right heart failure undergoing surgery (2022)

●Sixth WSPH: Paediatric pulmonary arterial hypertension – Updates on definition, classification, diagnostics, and management (2019)

●ISHLT: A scientific statement for evaluation and management of right-sided heart failure (2018)

●Pulmonary Vascular Research Institute (PVRI): Guidelines and consensus – A consensus approach to the classification of pediatric pulmonary hypertensive vascular disease (2011)

United States

●American Thoracic Society (ATS): Clinical practice guideline on interventional strategies for children with progressive pulmonary hypertension despite optimal therapy (2024)

●Pediatric Pulmonary Hypertension Network (PPHNet): An interdisciplinary consensus approach to pulmonary hypertension in developmental lung disease (2024)

●American College of Radiology (ACR): ACR Appropriateness Criteria on suspected pulmonary hypertension (2022)

●American Society of Hematology (ASH): Guidelines for sickle cell disease – Cardiopulmonary and kidney disease (2019)

●PPHNet: Evaluation and management of pulmonary hypertension in children with bronchopulmonary dysplasia (2017)

●Pediatric Cardiac Intensive Care Society (PCICS): Consensus statement – Pharmacotherapies in cardiac critical care pulmonary hypertension, 2014 (published 2016)

●PPHNet: Recommendations for the use of inhaled nitric oxide therapy in premature newborns with severe pulmonary hypertension (2016)

●American Heart Association (AHA)/ATS: Guideline on pediatric pulmonary hypertension (2015)

●ATS: Clinical practice guideline for the diagnosis, risk stratification, and management of pulmonary hypertension of sickle cell disease (2014)

Europe

●European Society of Cardiology (ESC)/European Respiratory Society (ERS): Guidelines for the diagnosis and treatment of pulmonary hypertension (2022)

●European Pediatric Pulmonary Vascular Disease Network (EPPVDN): Updated consensus statement on the diagnosis and treatment of pediatric pulmonary hypertension (2019)

Japan

●[In Japanese] Japanese Circulation Society (JCS)/Japanese Pulmonary Circulation and Pulmonary Hypertension Society (JPCPHS): Guideline on the management of pulmonary thromboembolism, deep venous thrombosis, and pulmonary hypertension (2025)

●[In English] Japanese Circulation Society (JCS): Guidelines for the treatment of pulmonary hypertension (2017)