Society guideline links: Motor neuron disease

Introduction — This topic includes links to society and government-sponsored guidelines from selected countries and regions around the world. We will update these links periodically; newer versions of some guidelines may be available on each society's website. Some societies may require users to log in to access their guidelines.

The recommendations in the following guidelines may vary from those that appear in UpToDate topic reviews. Readers who are looking for UpToDate topic reviews should use the UpToDate search box to find the relevant content.

Links to related guidelines are provided separately. (See "Society guideline links: Spinal muscular atrophy".)

International

●Primary lateral sclerosis – Consensus diagnostic criteria (2020)

●World Federation of Neurology (WFN): A revision of the El Escorial criteria (2015)

●Electrodiagnostic criteria for diagnosis of ALS (2008)

Canada

●Amyotrophic Lateral Sclerosis Society of Canada (ALS Canada): Canadian best practice recommendations for the management of amyotrophic lateral sclerosis (2020)

United States

●American Academy of Neurology (AAN): Guideline on the care of the patient with amyotrophic lateral sclerosis – Drug, nutritional, and respiratory therapies, update (2009, reaffirmed 2020)

●AAN: Guideline on the care of the patient with amyotrophic lateral sclerosis – Multidisciplinary care, symptom management, and cognitive/behavioral impairment, update (2009, reaffirmed 2020)

●American College of Radiology (ACR): ACR Appropriateness Criteria on movement disorders and neurodegenerative diseases (revised 2019)

●Northeast Amyotrophic Lateral Sclerosis Consortium (NEALS): Provisional best practices guidelines for the evaluation of bulbar dysfunction in amyotrophic lateral sclerosis (2019)

Europe

●European Society for Clinical Nutrition and Metabolism (ESPEN): Guideline clinical nutrition in neurology (2018)

●European Federation of Neurological Societies (EFNS): Guidelines on the clinical management of amyotrophic lateral sclerosis (MALS) (2012)

●EFNS: Guidelines for the molecular diagnosis of neurogenetic disorders – Motoneuron, peripheral nerve and muscle disorders (2011)

●EFNS: Guidelines on the use of neuroimaging in the management of motor neuron diseases (2010)

United Kingdom

●Royal College of Physicians (RCP): Supporting people who have eating and drinking difficulties – A guide to practical care and clinical assistance, particularly towards the end of life, 2nd edition (2021)

●National Institute for Health and Care Excellence (NICE): Guideline on motor neurone disease – Assessment and management (2016, updated 2019)

●NICE: Interventional procedures guidance on intramuscular diaphragm stimulation for ventilator-dependent chronic respiratory failure caused by motor neurone disease (2017)

●NICE: Quality standard on motor neurone disease (2016)

●Association for Palliative Medicine of Great Britain and Ireland (APM): Guidance for professionals on withdrawal of assisted ventilation at the request of a patient with motor neurone disease (2015)

●RCP, National Council for Palliative Care (NCPC), and British Society of Rehabilitation Medicine (BSRM): National guidelines on long-term neurological conditions – Management at the interface between neurology, rehabilitation and palliative care (2008)

Australia–New Zealand

●Motor Neurone Disease Australia (MND Australia): Motor neurone disease – Aspects of care for the primary health care team, 5th edition (2017)

Japan

●[In Japanese] Japanese Society of Neurology (JSN): Amyotrophic lateral sclerosis (ALS) clinical practice guidelines (2023)

●[In Japanese] A clinical manual on ALS and ALS-parkinsonism-dementia complex frequently occurring in the southern part of Kii Peninsula (2019)