Electron micrograph showing lamellar inclusions in distal tubular cells
Electron micrograph showing lamellar inclusions in distal tubular cells
Electron microscopy photomicrograph of distal tubules in a male patient with "classic" Fabry disease. The varied burden of globotriaosylceramide (Gb3) inclusions in distal tubular cells is illustrated by the relatively high level of inclusions in most cells (arrows) versus the relative paucity of inclusions in some cells (arrowhead).
Courtesy of Michael Mauer, MD.
Graphic 129381 Version 1.0
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