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خرید پکیج
تعداد آیتم قابل مشاهده باقیمانده : -1 مورد

CPAM types[1,2]

CPAM types[1,2]
Type 0 1 2 3 4
Proportion of CPAM cases 1 to 3% 60 to 70% 10 to 15% 5 to 10% 10 to 15%
Origin Tracheal or bronchial Distal bronchial or proximal bronchioles Terminal bronchioles Alveolar duct Distal acinar
Cyst size <0.5 cm 2 to 10 cm 0.5 to 2.0 cm
  • <0.5 cm cysts and solid-appearing areas or
  • Completely solid appearance
<7 cm
Comments
  • Diffuse malformation affecting entire lung
  • Lethal since lungs do not aerate at birth
  • Single lobe involved in 95% of cases
  • Rarely bilateral
  • Mediastinal shift and respiratory distress at birth can occur
  • Risk of bronchioloalveolar carcinoma
  • Usually one lobe involved
  • Associated malformations in 60% of cases, which may have worse prognosis than lung abnormality
  • Entire lobe or several lobes affected
  • Severe respiratory distress at birth
  • Usually one lobe involved
  • Respiratory distress at birth
  • Risk of pleuropulmonary blastoma
CPAM: congenital pulmonary airway malformation.
References:
  1. Gothi D, Joshi JM. A 38-year-old man with lung cysts. Ann Thorac Med 2011; 6:231.
  2. David M, Lamas-Pinheiro R, Henriques-Coelho T. Prenatal and Postnatal Management of Congenital Pulmonary Airway Malformation. Neonatology 2016; 110:101.
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