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خرید پکیج
تعداد آیتم قابل مشاهده باقیمانده : 3 مورد
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Frequency of specific cancer types in Werner syndrome*

Frequency of specific cancer types in Werner syndrome*
Frequent neoplasms
(67% of total)
Less common neoplasms
(33% of total)
Thyroid neoplasms (16%) Nonmelanoma skin cancer (5%)
Follicular thyroid carcinoma Squamous cell carcinoma
Papillary thyroid carcinoma Basal cell carcinoma
Anaplastic thyroid carcinoma Gastrointestinal (4%)
Thyroid adenoma Esophageal carcinoma
Malignant melanoma (13%) Gastric carcinoma
Acral lentiginous melanoma Pancreatic carcinoma
Malignant mucosal melanoma Uterus/ovary (4%)
Malignant melanoma nonacral lentiginous melanoma Ovarian cystadenocarcinoma
Meningioma (11%) Uterine carcinoma
Soft tissue sarcomas (10%) Uterine leiomyoma
Undifferentiated pleomorphic sarcoma (malignant fibrous histiocytoma) Hepatobiliary (4%)
Leiomyosarcoma Cholangiocarcinoma
Fibrosarcoma Hepatocellular carcinoma
Malignant peripheral nerve sheath tumor Genitourinary (4%)
Rhabdomyosarcoma Ureteral transition cell carcinoma
Synovial sarcoma Bladder transitional cell carcinoma
Hematologic/lymphoid (9%) Vulvar carcinoma
Acute myelogenous leukemia (M1 to M5, M6, M7) Prostate carcinoma
Preleukemic marrow disorders Head and neck neoplasms (3%)
Myelofibrosis Nasal carcinoma NOS
Myelodysplasia Hard/soft palate squamous cell carcinoma
Refractory anemia with excess blasts Tongue squamous cell carcinoma
T cell leukemia Laryngeal carcinoma
Plasmacytoma Breast carcinoma (3%)
Osteosarcoma/bone (8%) Lung (2%)
Osteoblastic osteosarcoma Squamous cell carcinoma
Fibroblastic osteosarcoma Adenocarcinoma
Extraskeletal/soft tissue osteosarcoma Bronchioloalveolar carcinoma
Osteochondroma Carcinoid
  CNS (2%)
  Astrocytoma
  Spinal cord hemangiolipoma
  Adrenal cortical (2%)
  Carcinoma
  Pheochromocytoma
NOS: not otherwise specified; CNS: central nervous system.
* Based on data from 189 patients with Werner syndrome.
From: Lauper JM, Krause A, Vaughan TL, Monnat RJ Jr. Spectrum and risk of neoplasia in Werner syndrome: a systematic review. PLoS One 2013; 8:e59709. Available at: https://journals.plos.org/plosone/article?id=10.1371/journal.pone.0059709. Copyright © 2013 The Authors. Reproduced under the terms of the Creative Commons Attribution License 4.0.
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