Brain imaging of a patient with Sturge-Weber syndrome and a left leptomeningeal capillary-venous malformation

A 61-year-old patient with Sturge-Weber syndrome and epilepsy. Noncontrast CT in transverse axial (A, B) and coronal (C) planes shows gyriform calcification underlying a leptomeningeal capillary-venous malformation (LCVM). On FLAIR (D) and T2-weighted (F) MRI, there is hyperintense signal in the sulci of the left occipital, parietal, and temporal lobes. Post-contrast MRI in the same planes (E, G) demonstrates linear enhancement of the LCVM that fills the subarachnoid spaces, covering the surfaces of the gyri and filling the cortical sulci. Also note enlargement of the choroid plexus in the left atrium (D, E) caused by blood shunted to the deep medullary veins that drain into the lateral ventricle.