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Acquired and potentially reversible causes of ataxia

Acquired and potentially reversible causes of ataxia
  Cerebellar ataxias Sensory ataxias
Immune mediated
  • Anti-GAD ataxia
  • Gluten ataxia
  • Multiple sclerosis
  • Paraneoplastic cerebellar degeneration (mainly in breast and ovary cancer, SCLC, Hodgkin lymphoma)
  • SREAT
  • Anti-MAG antibodies polyneuropathy
  • CANOMAD syndrome
  • CIDP
  • Guillain-Barré syndrome
  • MGUS-related neuropathy
  • Miller Fisher syndrome
  • Multiple sclerosis
  • Neurosarcoidosis
  • Paraneoplastic sensory neuropathies (breast and ovary cancer, bronchial carcinoma, Hodgkin lymphoma, neuroendocrine tumors, sarcoma, SCLC)
  • Sjögren's disease
Infections
  • Epstein-Barr virus (acute cerebellitis mainly in children and adults)
  • HIV
  • Lyme borreliosis
  • Syphilis
  • Varicella (acute cerebellitis mainly in children)
  • Whipple disease
  • Syphilis (tabes dorsalis)
Drugs
  • Alcohol*
  • Amiodarone
  • Antiseizure medications (phenytoin)
  • Asparaginase
  • Barbiturates
  • Benzodiazepines
  • Bismuth
  • Bromides
  • Calcineurin inhibitors (tacrolimus)
  • Capecitabine
  • Cytarabine
  • Fluorouracil
  • Glucocorticoids (high doses)
  • Lithium
  • Metronidazole
  • Phencyclidine
  • Piperazine
  • Zidovudine
  • Bortezomib
  • Carboplatin
  • CDDP
  • Cisplatin
  • Doxorubicin
  • Oxaliplatin
  • Penicillin
  • Suramin sodium
Metabolic
  • Deficiency of vitamin B1 (Wernicke encephalopathy)
  • Deficiency of vitamin E
  • Hypoparathyroidism
  • Hypothyroidism
  • Deficiency of vitamin B12
  • Deficiency of vitamin E
Structural lesions
  • Neoplasms
  • Stroke
  • Superficial siderosis
  • Spinal trauma/ischemia
  • Vertebrobasilar dolichoectasia
Toxins
  • Carbon tetrachloride
  • Lead
  • Manganese
  • Mercury
  • Toluene
  • Thallium

GAD: glutamic acid decarboxylase; SCLC: small cell lung cancer; SREAT: steroid-responsive encephalopathy associated with autoimmune thyroiditis (formerly known as Hashimoto encephalopathy); MAG: myelin-associated glycoprotein; CANOMAD: chronic ataxic neuropathy with ophthalmoplegia, immunoglobulin M (IgM) paraprotein, cold agglutinins, and disialosyl antibodies; CIDP: chronic inflammatory demyelinating polyneuropathy; MGUS: monoclonal gammopathy of undetermined significance; HIV: human immunodeficiency virus; CDDP: cis-diamminedichloroplatinum II.

* Chronic alcohol use disorder can cause irreversible alcoholic cerebellar degeneration.
Courtesy of Alfonso Fasano, MD, PhD, FAAN.
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