Anatomic location/morphology | Associated risk |
Facial, large segmental | PHACES syndrome (posterior fossa malformations, hemangiomas, arterial anomalies, cardiac defects, eye abnormalities, sternal clefting) |
Nasal tip, ear, large facial (especially with prominent dermal component) | Permanent scarring, disfigurement |
Periorbital and retrobulbar | Ocular axis occlusion, astigmatism, amblyopia, tear-duct occlusion |
Segmental "beard area," central neck | Airway hemangioma |
Perioral | Ulceration, disfigurement, feeding difficulties |
Segmental overlying lumbosacral spine | Tethered spinal cord, genitourinary anomalies |
Perineal, axilla, neck, perioral | Ulceration |
Multiple hemangiomas | Visceral involvement (especially liver, gastrointestinal tract) |
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