Affected system | Diagnosis | Manifestation |
Dermatologic | SLE | Malar rash and hair loss |
Dermatomyositis | Gottron's papules | |
Systemic JIA | Evanescent, pink macular rash | |
IgAV (HSP) | Lower-extremity purpuric lesions | |
Parvovirus | "Slapped cheek" erythema | |
ARF | Erythema marginatum | |
Kawasaki disease | Ranging from nonspecific erythema to subcutaneous edema and skin peeling | |
Ophthalmologic | Oligoarthritis or psoriatic JIA | Asymptomatic chronic anterior uveitis |
Enthesitis related arthritis | Acute symptomatic uveitis (pain, redness) | |
Kawasaki disease | Conjunctival injection without discharge | |
Sjögren's syndrome | Dry eyes with keratitis | |
Oral | SLE | Painless oral ulcers on palate |
Behçet disease | Large, extremely painful oral ulcers | |
Kawasaki disease | Mucositis and strawberry tongue | |
Respiratory | CF or immunodeficiency | Recurrent pneumonia |
Granulomatosis with polyangiitis | Destructive upper tract lesions | |
SLE or systemic JIA | Pleuritis | |
SLE or scleroderma | Interstitial lung disease | |
Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) | Eosinophilic pneumonia | |
Cardiovascular | ARF or endocarditis | New heart murmur |
SLE, systemic JIA, or ARF | Pericarditis | |
SLE or scleroderma | Raynaud phenomenon | |
Takayasu arteritis | Absent pulses | |
Kawasaki disease | Carditis, coronary artery aneurysms | |
Gastrointestinal | IBD, SLE, vasculitis, leukemia, lymphoma, or other malignancy | Weight loss or poor growth |
IBD | Diarrhea and abdominal pain | |
Reactive arthritis | Preceding infectious gastroenteritis | |
IgAV (HSP) | Intermittent colicky abdominal pain | |
Periodic fevers (FMF, PFAPA) | Abdominal pain during fever episodes | |
Genitourinary | Gonococcal arthritis | Pustular urethritis or cervicitis |
Reactive arthritis | Nongonococcal urethritis | |
Behçet disease or IBD | Large, painful genital ulcerations | |
Hematologic | SLE or hemoglobinopathy (eg, SCD) | Pancytopenia, hemolytic anemia |
Leukemia, lymphoma | Cytopenias, blasts on smear | |
Bleeding disorders | Hemarthrosis | |
Neurologic | SLE | Seizures and psychosis |
SLE or fibromyalgia | Difficulty concentrating | |
SLE, vasculitis, or hypercoagulability | Stroke | |
Vasculitis, including Kawasaki disease | Asymmetric polyneuropathy, severe irritability | |
Dermatomyositis and polymyositis | Proximal muscle weakness |
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