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تعداد آیتم قابل مشاهده باقیمانده : -47 مورد

Classification of autoimmune hemolytic anemia

Classification of autoimmune hemolytic anemia
Warm-reactive AIHA
Primary*
Secondary
  • Autoimmune or inflammatory disorders (eg, systemic lupus erythematosus, Sjögren syndrome, scleroderma, juvenile idiopathic arthritis, dermatomyositis, vitiligo, ulcerative colitis, autoimmune hepatitis, type 1 diabetes mellitus, autoimmune thyroiditis)
  • Evans syndrome
  • Primary immunodeficiency (eg, common variable immune deficiency, Wiskott-Aldrich syndrome)
  • Acquired immunodeficiency (eg, HIV)
  • Malignancy (eg, acute leukemia, lymphoma, chronic lymphocytic leukemia)
  • InfectionΔ
  • Posttransplant
Cold agglutinin disease
Primary*
Secondary
  • Infection (eg, Mycoplasma pneumoniae, EBV)Δ
  • Malignancy (eg, lymphoma)
Paroxysmal cold hemoglobinuria
Primary
Post-infectiousΔ
Refer to UpToDate for details of the evaluation and management.

AIHA: autoimmune hemolytic anemia; EBV: Epstein-Barr virus.

* Primary AIHA refers to disorders with only immune-mediated hemolytic anemia and no evidence of an underlying systemic disorder.

¶ Secondary AIHA refers to disorders with immune-mediated hemolytic anemia in the presence of another condition. Common secondary causes are listed in this table. For further details, refer to UpToDate content on AIHA in children.

Δ Infectious and post-infectious causes of AIHA are most commonly associated with cold agglutinins disease and paroxysmal cold hemoglobinuria.
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