Idiopathic pulmonary fibrosis (UIP pattern required to confirm the diagnosis) |
Asbestosis |
Chronic aspiration pneumonia |
Connective tissue diseases |
UIP-like reaction (associated with other specific histologic findings) |
Hypersensitivity pneumonitis |
Lymphocytic interstitial pneumonia |
Chronic radiation pneumonitis |
Chronic eosinophilic pneumonia |
Infections |
Hemosiderosis |
Hermansky-Pudlak syndrome |
Neurofibromatosis |
Alveolar proteinosis |
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