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Etiology of arrhythmias in congenital heart disease

Etiology of arrhythmias in congenital heart disease
Bradycardia Examples
Congenital
Congenital sinus node dysfunction Situs inversus
Congenital AV block AV canal defects; cc-TGA
Acquired
Acquired sinus node dysfunction s/p repair of Mustand/Senning, Fontan, Glenn or sinus venosus ASD
Acquired AV node dysfunction s/p VSD/LVOT/aortic valve operation
Tachycardia Examples
Congenital
Twin AV nodes Heterotaxy syndrome
Acquired
Atrial tachycardia/flutter Atrial baffles; post-MAZE
Atrial fibrillation ASD's, mitral valve disease
Ectopic atrial tachycardia Fontan
AV: atrioventricular; cc-TGA: congenitally corrected transposition of the great arteries; ASD: atrial septal defect; VSD: ventricular septal defect; LVOT: left ventricular outflow tract.
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