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Causes of fever of unknown origin in children

Causes of fever of unknown origin in children
Generalized infections
Most common causes:
  • Cat scratch disease
  • Malaria
  • Salmonella
  • Tuberculosis
  • Viral infection (CMV, EBV, adenovirus)
Less common causes:
  • Brucellosis
  • Leptospirosis
  • Toxoplasmosis
  • Tularemia
Rare causes:
  • Arbovirus
  • Enterovirus
  • Fungal infections (nonpulmonary blastomycosis, disseminated histoplasmosis)
  • Hepatitis viruses
  • HIV
  • Lymphogranuloma venereum
  • Psittacosis
  • Q fever
  • Rocky Mountain spotted fever
  • Visceral larva migrans
Localized infections
  • Infective endocarditis
  • Intra-abdominal abscess (hepatic, perinephric, pelvic, subdiaphragmatic)
  • Liver infection (eg, bacterial cholangitis, granulomatous hepatitis)
  • Osteomyelitis and septic arthritis (less frequently)
  • Upper respiratory infection: Chronic or recurrent otitis media, chronic or recurrent pharyngitis, mastoiditis, peritonsillar abscess, sinusitis
  • Urinary tract infection
Rheumatologic diseases
  • Juvenile idiopathic arthritis
  • Systemic lupus erythematosus
  • Vasculitis (eg, polyarteritis nodosa, Henoch-Schönlein purpura)
Malignancies
Most common causes:
  • Leukemia
  • Lymphoma
Less common causes:
  • Atrial myxoma
  • Hepatoma
  • Neuroblastoma
  • Sarcoma
Miscellaneous
  • Central nervous system dysfunction
  • Diabetes insipidus (central or nephrogenic)
  • Drug fever
  • Ectodermal dysplasia
  • Factitious fever
  • Familial dysautonomia
  • Granulomatous colitis
  • Hemophagocytic lymphohistiocytosis
  • Immunodeficiency
  • Infantile cortical hyperostosis
  • Inflammatory bowel disease
  • Kawasaki disease
  • Kikuchi disease
  • Multisystem inflammatory syndrome in children
  • Pancreatitis
  • Periodic fever (eg, Mediterranean fever, PFAPA syndrome)
  • Sarcoidosis
  • Serum sickness
  • Thyrotoxicosis
CMV: cytomegalovirus; EBV: Epstein-Barr virus; PFAPA: periodic fever with aphthous stomatitis, pharyngitis, and adenitis.
Modified from: Lorin MI, Feigin RD. Fever without localizing signs and fever of unknown origin. In: Textbook of Pediatric Infectious Disease, 4th ed, Feigin RD, Cherry JD (Eds), WB Saunders, Philadelphia 1998, with permission from Elsevier Science.
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