Normal response to ischemic exercise | Lactate | Pyruvate | Ammonia |
3- to 5-fold increase | 3- to 5-fold increase | 5- to 10-fold increase | |
Glycolytic/glycogenolytic defects | No rise or <2-fold increase | No rise or <2-fold increase | Normal |
Except: | |||
Phosphorylase b kinase deficiency | Normal - mildly increased | Normal - mildly increased | Normal |
Acid maltase deficiency | Normal | Normal | Normal |
Lactate dehydrogenase deficiency | No rise | Normal to markedly increased | Normal |
Fatty acid oxidation defects | Normal | Normal | Normal |
Mitochondrial defects | Normal to increased | Normal to increased | Normal |
Myoadenylate deficiency | Normal | Normal | No rise |
آیا می خواهید مدیلیب را به صفحه اصلی خود اضافه کنید؟