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Features distinguishing spasmus nutans from congenital nystagmus

Features distinguishing spasmus nutans from congenital nystagmus
  Congenital nystagmus Spasmus nutans
Features of nystagmus
Waveform Often mixed with jerk Strictly pendular
Amplitude Large, always >3° Small, often <3°
Amplitude asymmetry Minimal (<25 percent) >25 percent
Frequency Slow, <7Hz Fast, >7Hz
Phase relationship Conjugate Dysconjugate
Duration Constant Intermittent
Other features
Age at onset <6 months >6 months
Associated strabismus/amblyopia   More frequent
Head nodding   Larger and more frequent
Horizontal OKR Absent or inverted Normal
Data from: Gottlob I, Zubcov A, Catalano RA, et al. Ophthalmology 1990; 97:1166.
Graphic 76335 Version 3.0

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