Supravalvar aortic stenosis catheter angiogram

Discrete supravalvar aortic stenosis in a patient with Williams syndrome. This catheter angiogram in an anteroposterior projection with contrast injection in the aortic root demonstrates the typical discrete narrowing of the ascending aorta at the sinotubular junction (arrow), just above the aortic sinuses of Valsalva. This angiogram is also clinically useful to exclude the more severe manifestations of the aortopathy seen with Williams syndrome, demonstrating no stenoses of the coronary artery origins, proximal brachiocephalic vessels, or hypoplasia/coarctation of the thoracic aorta.