Erythrodontia in congenital erythropoietic porphyria (CEP)

Brownish discolored teeth fluoresce (erythrodontia) when exposed to ultraviolet light. The erythrodontia is the result of the accumulation of uroporphyrin I and coproporphyrin I in the patient's teeth.

Reproduced with of American Society of Hematology, from: Balwani M, Desnick RJ. The porphyrias: advances in diagnosis and treatment. Blood 2012; 120:4496; permission conveyed through Copyright Clearance Center, Inc.

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