ﺑﺎﺯﮔﺸﺖ ﺑﻪ ﺻﻔﺤﻪ ﻗﺒﻠﯽ
خرید پکیج
تعداد آیتم قابل مشاهده باقیمانده : 3 مورد
نسخه الکترونیک
medimedia.ir

Sunflower syndrome

Sunflower syndrome
Epidemiology Incidence unknown; occurs more frequently in girls
Age at onset First decade
Semiology Unilateral hand waving* with or without head movement towards light, with or without eyelid myoclonia, with or without impairment of awareness
Precipitants Natural light more than artificial light
Seizure frequency Frequent – up to multiple times daily
Additional seizure types Absence, atypical absence, tonic-clonic, myoclonic, and atonic
Associated features Heliotropism* and photosensitivity
Cognition Often normal, but may be associated with ADHD or intellectual disability
Family history of seizures/epilepsy Variable (approximately 30 to 50%)
Typical interictal EEG findings Generalized epileptiform discharges at 1 to 4 Hz and normal background activity with or without photoparoxysmal response and hyperventilation-induced epileptiform discharges
Typical ictal EEG findings Generalized epileptiform discharges at 3 to 4 Hz
Typical neuroimaging findings Normal
Select differential diagnoses Jeavons syndrome, tic disorders, and behavioral issues
Pharmacologic treatments Broad spectrum antiseizure medications such as valproate, lamotrigine, and levetiracetam
Non-pharmacologic treatments Dietary therapy, avoid triggers, wear sunglasses or tinted glasses, wear hat, eye patch (closure of one eye)
Seizure outcomes Usually drug-resistant

ADHD: Attention deficit-hyperactivity disorder.

* Features that distinguish Sunflower syndrome from Jeavons syndrome.
References:
  1. Aicardi J, Gastaut H. Treatment of self-induced photosensitive epilepsy with fenfluramine. N Engl J Med 1985; 313:1419.
  2. Ames FR. "Self-induction" in photosensitive epilepsy. Brain 1971; 94:781.
  3. Ames FR, Saffer D. The sunflower syndrome. A new look at "self-induced" photosensitive epilepsy. J Neurol Sci 1983; 59:1.
  4. Andermann K. Berman S, Cooke PM, et al. Self-induced epilepsy. A collection of self-induced epilepsy cases compared with some other photoconvulsive cases. Arch Neurol 1962; 6:49.
  5. Barnett JR, Fleming BM, Geenen KR, et al. Characterizing sunflower syndrome: a clinical series. Epileptic Disord 2020; 22:273.
  6. Baumer FM, Porter BE. Clinical and electrographic features of sunflower syndrome. Epilepsy Res 2018; 142:58.
  7. Belcastro V, Striano P. Self-induction seizures in sunflower epilepsy: a video-EEG report. Epileptic Disord 2014; 16:93.
  8. Binnie CD. Self-induction of seizures: the ultimate non-compliance. Epilepsy Res 1988; 1:153.
  9. Caraballo RH, Fontana E, Darra F, et al. A study of 63 cases with eyelid myoclonia with or without absences: type of seizure or an epileptic syndrome? Seizure 2009; 18:440.
  10. Hutchinson JH, Stone FH, Davidson JR. Photogenic epilepsy induced by the patient. Lancet 1958; 1:243.
  11. Roberston EG. Photogenic epilepsy: self-precipitated attacks. Brain 1954; 77:232.
  12. Striano S, Capovilla G, Sofia V, et al. Eyelid myoclonic with absences (Jeavons syndrome): a well-defined idiopathic generalized epilepsy syndrome or a spectrum of photosensitive conditions? Epilepsia 2009; 50:15.
Graphic 130466 Version 1.0

آیا می خواهید مدیلیب را به صفحه اصلی خود اضافه کنید؟