Version July 2025
| Considerations when applying these criteria | |
| |
| Absolute requirements | |
| Age ≤60 years at time of diagnosis | |
| Evidence of vasculitis on imaging* | |
| Additional clinical criteria | |
| Female sex | +1 |
| Angina or ischemic cardiac pain | +2 |
| Arm or leg claudication | +2 |
| Vascular bruit¶ | +2 |
| Reduced pulse in upper extremityΔ | +2 |
| Carotid artery abnormality◊ | +2 |
| Systolic blood pressure difference in arms ≥20 mmHg | +1 |
| Additional imaging criteria | |
| Number of affected arterial territories (select one)§ | |
| +1 |
| +2 |
| +3 |
| Symmetric involvement of paired arteries¥ | +1 |
| Abdominal aorta involvement with renal or mesenteric involvement‡ | +3 |
* Evidence of vasculitis in the aorta or branch arteries must be confirmed by vascular imaging (eg, computed tomographic/catheter-based/magnetic resonance angiography, ultrasound, positron emission tomography).
¶ Bruit detected by auscultation of a large artery, including the aorta, carotid, subclavian, axillary, brachial, renal, or iliofemoral arteries.
Δ Reduction or absence of pulse by physical examination of the axillary, brachial, or radial arteries.
◊ Reduction or absence of pulse of the carotid artery or tenderness of the carotid artery.
§ Number of arterial territories with luminal damage (eg, stenosis, occlusion, or aneurysm) detected by angiography or ultrasonography from the following 9 territories: thoracic aorta, abdominal aorta, mesenteric, left or right carotid, left or right subclavian, left or right renal arteries.
¥ Bilateral luminal damage (stenosis, occlusion, or aneurysm) detected by angiography or ultrasonography in any of the following paired vascular territories: carotid, subclavian, or renal arteries.
‡ Luminal damage (stenosis, occlusion, aneurysm) detected by angiography or ultrasonography involving the abdominal aorta and either the renal or mesenteric arteries.